Chordoma arising from the coccygeal disc and mimicking a pilonidal cyst.

Publication Type	Case Report
Authors	Mazzucco M, Hwang S, Linos K, Hameed M, Shahzad F, Schmitt A, Boland P, Vaynrub M
Journal	Skeletal Radiol
Volume	53
Issue	7
Pagination	1431-1435
Date Published	11/13/2023
ISSN	1432-2161
Keywords	Pilonidal Sinus, Chordoma, Sacrococcygeal Region
Abstract	Chordomas are rare, low-grade malignant tumors often found in the sacrococcygeal region and prone to local recurrence. We report an atypical presentation of a 40-year-old patient with a symptomatic midline retrococcygeal lesion that was presumptively treated as a pilonidal cyst due to its clinical and imaging features. After surgical pathology rendered the diagnosis of chordoma, the patient required salvage surgery in the form of partial sacrectomy with soft tissue flap coverage. In addition to the unusually predominant retrococcygeal location, surgical pathology identified an intervertebral disc origin rather than the typical osseous origin. To our knowledge, this presentation of chordoma with coccygeal intervertebral origin and a large subcutaneous mass at imaging has rarely been reported in the literature. We describe this case to raise awareness of atypical presentations of sacrococcygeal chordoma that may lead to erroneous presumptive diagnosis and treatment.
DOI	10.1007/s00256-023-04492-4
PubMed ID	37953332
PubMed Central ID	PMC11879305